Acral papular mucinosis: a new case of this rare entity*
نویسندگان
چکیده
Acral persistent papular mucinosis (APPM) is a rare subtype of localized lichen myxedematosus. It consists of small papules localized exclusively on the back of the hands, wrists and extensor aspects of distal forearms with no other clinical or laboratory manifestations. The lesions tend to persist and may increase slowly in number. Histologically, hematoxylin-eosin and Alcian blue staining demonstrate mucin accumulation in the upper reticular dermis with separation of collagen fibers as a result of hyaluronic acid deposition. Treatment is rarely necessary due to the absence of symptoms. We present a 27-year-old healthy woman with asymptomatic papules on her upper extremities, which adequately meet clinical and pathological criteria of acral papular mucinosis.
منابع مشابه
Discrete ('acral nonpapular') localised lichen myxedematosus.
To cite: Reserva J, Marchalik R, Braniecki M. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/ bcr-2015-209462 DESCRIPTION Localised lichen myxedematosus (LM) is a chronic idiopathic papular mucinosis that can be divided into five subtypes: a discrete papular (DPLM) form, acral persistent papular mucinosis (APPM), papular mucinosis of infancy, a nodular form and selfh...
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